Type A (~33%): Interruption occurs after the aortic isthmus, just beyond the left subclavian artery and proximal to the ductal insertion. There are three subtypes which are classified according to the site of the interruption: This is infrequently seen with type A or C. IAA type B is specifically associated with a posterior malalignment ventricular septal defect (VSD) with resultant narrowing of the left ventricular outflow tract (LVOT) and hypoplasia of the aortic valve.Īmong patients with congenital heart disease, IAA occurs ~1% of the time, with IAA type B being the most common form.Īmong patients with IAA, specifically type B, >50% have 22q11 deletion (DiGeorge syndrome). Interrupted aortic arch (IAA) is a congenital anomaly where there is interruption or discontinuation of a segment of the aortic arch. IAA is frequently associated with ventricular septal defects (VSD) and a bicuspid aortic valve. Left Ventricular Non Compaction Cardiomyopathy (LVNC).Right Aortic Arch with an Aberrant Left Subclavian Artery (Vascular Ring).Infracardiac Total Anomalous Pulmonary Venous Return.Idiopathic Infantile Arterial Calcification.Congenitally Corrected Transposition of the Great Arteries (ccTGA).Transposition of the Great Arteries (DTGA).Pulmonary Atresia with Intact Ventricular Septum (PA/IVS).Tetralogy of Fallot with Pulmonary Atresia.Tetralogy of Fallot with Absent Pulmonary Valve.Supracardiac Total Anomalous Pulmonary Venous Return.Total Anomalous Pulmonary Venous Return to the Coronary Sinus.Pulmonary Artery Sling (Vascular Sling).Anomalous Left Coronary Artery from the Right Coronary Artery.Anomalous Right Coronary Artery from the Left Coronary Artery.

Transitional Atrioventricular Canal (AV Canal).Partial Atrioventricular Canal (AV Canal).Complete Atrioventricular Canal (AV Canal).

Interrupted aortic arch syndrome